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產(chǎn)品基本信息
產(chǎn)品編號(hào):P155054
產(chǎn)品名稱:Palmitoyl-L-carnitine-13C3 Hydrochloride
產(chǎn)品CAS:
規(guī)格含量:2.5mg
產(chǎn)品價(jià)格:面議
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產(chǎn)品詳細(xì)介紹
標(biāo)準(zhǔn)品編號(hào):
P155054
名稱:
Palmitoyl-L-carnitine-13C3 Hydrochloride
別名:
(2R)-3-Carboxy-N,N,N-trimethyl-2-[(1-oxohexadecyl)oxy]-1-propanaminium Chloride13C3; L-(3-Carboxy-2-hydroxypropyl)trimethyl-ammonium Chloride Palmitate13C3; L-Palmitic acid ester with (3-carboxy-2-hydroxypropyl)trimethylammonium chloride13C3; (-)-(3-Carboxy-2-hydroxypropyl)trimethyl-ammonium Chloride Palmitate13C3; Hexadecanoyl-L-carnitine hydrochloride13C3; L-Palmitoylcarnitine chloride13C3
參考CAS號(hào):
Unlabelled: 18877-64-0
分子式:
C??¹³C?H??ClNO?
分子量:
438.04
類別:
Standards; Isotopic Labeled Analogues; Lipids/Fatty Acids, Glycerol Derivatives;
應(yīng)用:
Palmitoyl-L-carnitine-13C3 Hydrochloride is carbon-13 labeled Palmitoyl-L-carnitine Hydrochloride (P155050), a long-chain fatty ester of carnitine which is accumulated and released into the circulation, in fatty-acid oxidation defects. Pattern of Lauroyl-L-carnitine can be diagnostic for a number of ß-oxidation defects.
參考文獻(xiàn)
Ventura, F., et al.: Clinica Chimica Acta, 281, 1 (1999); Pourfarzam, M., et al.: Clinical Chem,, 40, 2267 (1994); Schaefer, J., et al.: Pediatric Res., 37, 354 (1995)