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產(chǎn)品基本信息
產(chǎn)品編號(hào):E922020
產(chǎn)品名稱:Ethylmalonic Acid
產(chǎn)品CAS:601-75-2
規(guī)格含量:10g
產(chǎn)品價(jià)格:面議
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產(chǎn)品詳細(xì)介紹
標(biāo)準(zhǔn)品編號(hào):
E922020
名稱:
Ethylmalonic Acid
別名:
Ethyl-propanedioic Acid; 1,1-Propanedicarboxylic Acid; 2-Ethylpropanedioic Acid;Ethylmalonic Acid; NSC 96615; α-Carboxybutyric Acid
CAS號(hào):
601-75-2
分子式:
C?H?O?
外觀:
白色固體
熔點(diǎn):
107-110°C
分子量:
132.11
儲(chǔ)存:
-20°C Freezer
溶解度:
DMSO (Slightly), Methanol (Slightly)
種類:
Building Blocks; Miscellaneous;
應(yīng)用:
Ethylmalonic Acid is used as a diagnostic agent used in the diagnosis of Ethylmalonic encephalopathy which is a rare autosomal recessive inborn error of metabolism.
參考文獻(xiàn)
Baertling, F. et al.: Eur. J. Pediat., 173, 1719 (2014); Sudo, Y. et al.: Hu,am Genome Var., 1, 15016 (2014);